Epistaxis como primeira manifestação de granulomatose Wegener. Caso clínico

Autores

  • A. Casas Novas Interna Complementar de Otorrinolaringologia, do Centro Hospitalar Lisboa Central, EPE, Hospital Dona Estefânia
  • I. Moreira Interna Complementar de Otorrinolaringologia, do Centro Hospitalar Lisboa Central, EPE, Hospital Dona Estefânia
  • P. Brazão Santos Assistente Hospitalar de Otorrinolaringologia, do Centro Hospitalar Lisboa Central, EPE, Hospital Dona Estefânia
  • L. Monteiro Directora de Serviço de Otorrinolaringologia do Centro Hospitalar Lisboa Central, EPE, Hospital Dona Estefânia

DOI:

https://doi.org/10.34631/sporl.271

Palavras-chave:

epistaxis, Granulomatose Wegener, vasculite, granuloma

Resumo

A Granulomatose de Wegener é uma doença sistémica de etiologia desconhecida, caracterizada pela tríade clínica: envolvimento da mucosa nasal e dos seios perinasais, infiltração e cavitação pulmonar e doença renal com hematúria. A Granulomatose de Wegener afecta normalmente adultos jovens e de meia idade e embora seja incomum nas crianças, pode surgir em qualquer estrato etário.

Apresentamos o caso clínico de uma adolescente de 14 anos, com sintomas de epistaxis, cuja investigação posterior mostrou insuficiência renal e múltiplos nódulos pulmonares. O teste positivo para o anticorpo antineutrofílico citoplasmático suportou o diagnóstico de Granulomatose de Wegener, necessitando de terapêutica com hemodiálise e imunossupressão.

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Como Citar

Casas Novas, A., Moreira, I., Brazão Santos, P., & Monteiro, L. (1). Epistaxis como primeira manifestação de granulomatose Wegener. Caso clínico. Revista Portuguesa De Otorrinolaringologia E Cirurgia De Cabeça E Pescoço, 48(2), 89-92. https://doi.org/10.34631/sporl.271

Edição

Secção

Caso Clínico