Linfoma T/NK extranodal tipo nasal de localização atípica na orofaringe

Autores

  • Ana Guimarães Interna do Internato Complementar do Serviço de ORL do Hospital Fernando Fonseca
  • Ana Hebe Interna do Internato Complementar do Serviço de ORL do Hospital Fernando Fonseca
  • Filipe Freire Assistente Hospitalar do Serviço de ORL do Hospital Fernando Fonseca
  • João Prata Chefe de Serviço do Serviço de ORL do Hospital Fernando Fonseca
  • Gabão Veiga Director do Serviço de ORL do Hospital Fernando Fonseca

DOI:

https://doi.org/10.34631/sporl.251

Palavras-chave:

Linfoma T/NK, orofaringe

Resumo

O linfoma de células T/NK constitui um subtipo raro de linfoma nasosinusal, previamente conhecido por granuloma letal da linha média, caracterizando-se pela destruição progressiva das estruturas medio-faciais. Existe uma forte associação com a infecção pelo vírus Epstein-Barr. Apresenta-se o caso clínico de uma mulher de 43 anos com linfoma T/NK extranodal do tipo nasal com localização atípica na orofaringe. Apesar da sua raridade, existem actualmente esquemas terapêuticos bem definidos. Contudo, o prognóstico permanece geralmente desfavorável.

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Como Citar

Guimarães, A., Hebe, A., Freire, F., Prata, J., & Veiga, G. (1). Linfoma T/NK extranodal tipo nasal de localização atípica na orofaringe. Revista Portuguesa De Otorrinolaringologia E Cirurgia De Cabeça E Pescoço, 47(3), 213-217. https://doi.org/10.34631/sporl.251

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